As a child, doctors thought I might have VonWillebrand disease. As an adult, I've been diagnosed with Vascular EDS. Is this common?

In childhood many individuals with Vascular EDS are first thought to have a coagulation disorder. Bleeding disorders can arise from disorders of the vessel wall defects, platelets and coagulation. There are some patients with EDS, however, who have been diagnosed with Von Willebrand, Factor deficiencies and even Haemophilia. Most laboratory studies reveal bleeding and clotting times to be normal, even though most require blood transfusions and intravenous alimentation. Recent studies have shown that the increased bleeding tendency probably is due to a defect in the collagen structure of the vascular and perivascular tissues. Possible capillary fragility and venous varicosities may also occur. There is also a reduction in the ability of abnormal collagen in patients with EDS to attract platelets, which may contribute to the bleeding tendency. [Karaca et al. "Abnormal platelet collagen reaction in EDS" J Haematol 1972; 9:465–9. Wesley TA. "Multiple surgical problems in two patients with EDS" Surgery 1980;87 (3): 319–24]

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